Anatomical observations of the persistent urogenital sinus in virilized females due to congenital adrenal hyperplasia.

Citation:
Marei M, Fares AE, Abdelsattar AH, Hassan MM, Seif H, El-Kotby M, et al. Anatomical observations of the persistent urogenital sinus in virilized females due to congenital adrenal hyperplasia.. In: British Association of Paediatric Surgeons. Edinburgh; 2014. copy at www.tinyurl.com/hunprer

Date Presented:

July 2014

Abstract:

Virilized females due to congenital adrenal hyperplasia present the most common form of female DSD. The anomaly is an external virilization resembling male genitalia and a persistent urogenital sinus. The length of the proximal urethra, measured from the bladder neck to the vaginal-urethral confluence is an important predictor of surgical complexity. As the reconstruction is through a perineal approach, the vertical depth of the confluence from the perineum is similarly an important measurement. It determines the amount of the dissection required to deliver the vagina. There is no reported description of this level or depth, hence we present the measurements found in our series, and suggest a method to assess the difficulty of cases by applying a calculated ratio.

British Association of Paediatric Surgeons, Edinburgh, BAPS 61st Annual Congress

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DOI:

10.13140/2.1.2220.8643

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